Colloid cysts are benign tumor arising from third ventricle, very rare in children. Unlike in adults they present with aggressive behavior due to their rapid growth of tumor, late detection, and rapid development of the manifestations in children. Clinical features vary from asymptomatic to acute obstruction of third ventricle, leading to sudden death.

Keywords: Colloid Cyst; Third Ventricle; Acute Hydrocephalus; Sudden Death.