Encephalocele represents herniation of cranial contents through a congenital defect in the cranium.Herniation of cerebrospinal fluid (CSF) and meninges , is termed as a meningocele. A meningoencephalocele is herniation of both neural elements and meninges. There are various anaesthetic challenges in management of occipital meningoencephalocele these include securing the airway with intubation in lateral position, intraoperative prone position and complications associated with it , careful securing of the endotracheal tube and accurate assessment of blood loss. We report a case of a giant occipital meningoencephalocele and discuss its treatment.

Keyword: Meningoencephalocele.