Moyamoya disease is a cerebrovascular occlusive disease of rare incidence. We report a case series of 8 patients who were diagnosed as Moyamoya disease at a tertiary care hospital. Median age of presentation was 6 years. Stroke was the commonest presentation. Neuroimaging revealed bilateral vascular involvement in all 8 patients. In one patient there was associated involvement of common carotid artery and vertebral artery. Only 2 patients underwent surgery, remaining were managed conservatively. All the patients left with neurological deficits. Conservative management (aspirin/ calcium channel blockers/ physiotherapy), and surgical revascularization procedures are the mainstay of treatment.

Keywords: Moyamoya; Stroke; Magnetic Resonance Angiography.