Giant interhemispheric arachnoid cysts are rare lesions. These are generally associated with midline neurodevelopmental anomalies as seen in aforementioned case (2, 3). Treatment of these lesions is controversial. None of the surgical techniques described has proven superiority over others. Conservative management can be considered irrespective of the size in cysts with no change in size or raised ICP. We are reporting a case of giant intracranial interhemispheric arachnoid cyst in a 2year old male child.

Key words: Giant interhemispheric; Arachnoid cysts; Neurodevelopmental anomalies.