Ventriculo-peritoneal (VP) shunt is a procedure performed for diverting the cerebrospinal fluid (CSF) flow in patients with hydrocephalus. The procedure may be associated with various complications including mechanical complications (shunt block, shunt obstruction or shunt migration) and biological complications (shunt infection). CSF pseudocyst, commonly called “CSFoma” is a rare but significant
complication of VP shunt. We present a case of Crouzon syndrome (with hydrocephalus) operated for VP shunt, who developed a CSF pseudocyst within 3 months of insertion of the VP shunt. He presented
with abdominal distension and the diagnosis was confirmed by ultrasonography followed by a contrast enhanced computed tomographic (CECT) scan of the abdomen. The patient underwent therapeutic fluid tapping for the abdominal distension (as it was causing respiratory distress) followed by exteriorisation of the VP shunt till the pseudocyst resolved. The VP shunt was replaced later with a ventriculo-atrial shunt. The child has been doing well with no further complications at 4 weeks of follow-up.

Keywords: Abdominal pseudocyst; Crouzon syndrome; CSFoma; Hydrocephalus; Ventriculoperitoneal shunt.