Abstract Adrenocortical carcinoma (ACC) is a rare neoplasm with poor prognosis. Discriminating benign and malignant behaviour is more challenging. We report a case of adrenocortical adenoma (ACA) and two cases of adrenocortical carcinoma (ACC). All three cases were girls and presented with features of virilisation. Tumour weight, size, and Weiss criteria were found to be useful clinicopathological criteria for distinguishing adenoma from carcinoma.
Keywords: Adrenocortical Adenoma; Adrenocortical Carcinoma; Hirsutism.