Background: The Omental fibrous hamartoma is a very rare lesion, mainly seen in children characterised by single/multiple, Omental/mesenteric large solid mass, which may be confused with malignant neoplasm.Microscopically these are composed of fibroblast in bundles separated by myxomatous stroma. Lesion has benign clinical course without recurrence.Case Presentation: We present a 3 yrs old male child with history of complaints of abdominal lump since 2 yrs, which was increasing progressively in size over period of time. No history of nausea, vomiting, fever etc. Contrast enhanced computed tomography (CECT) revealed large well-demarcated heterogeneously hyperdense lesion in right hypochondriac, right lumbar and umbilical region displacing bowel loops on either side without penetration & showing minimal enhancement on contrast study. Histological examination of entire mass confirmed the diagnosis of OMENTAL FIBROUS MYXOID HAMARTOMA. No evidence of recurrence noted during follow up period of 2 yrs.Conclusion: Fibrous hamartoma of omentum is a very rare lesion and its aggressive appearance needs to differentiate from malignancy. The clinical picture of our case also led to high suspicion of malignancy.However by consideration of histological findings we could achieve the correct diagnosis.
: N.J. Gadekar